Lethal Midline Granuloma Presenting as Facial Cellulitis.
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Date
2009-01
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Abstract
Lethal midline granuloma (Midline granuloma, Midline reticulosis, Polymorphic reticulosis, and Angiocentric
immunoproliferative lesion) is relatively a rare entity of unknown etiology characterized by a massive
destruction, erosion and mutilation of the tissues of nose and upper respiratory passages. Unlike Wagner’s
granulomatosis which is known for its multi organ involvement, lethal midline granuloma remains usually
localized. Without therapeutic intervention it has a very high mortality. Radiotherapy is the treatment of
choice which considerably improves both quality and quantity of life. Addition of chemotherapy gives
additional benefit. Sporadic cases have appeared in literature from time to time under various synonyms.
Description
Keywords
Lethal midline granuloma, Reticulosis, Wagner’s granulamatosis, Immunoproliferative lesion
Citation
Teli M Ashraf, K M Baba, Gupta Meenu, Arshad Syed, Katoch S S, Nazir Imran. Lethal Midline Granuloma Presenting as Facial Cellulitis. JK Science Journal of Medical Education and Research. 2009 Jan-Mar;11(1): 39-41