Severe Calcinosis Cutis with Cutaneous Ulceration in Juvenile Dermatomyositis.

Loading...
Thumbnail Image
Date
2014-11
Journal Title
Journal ISSN
Volume Title
Publisher
Abstract
Background: Calcinosis cutis is usually seen in long standing and untreated cases of juvenile dermatomyositis. Case characteristics: 7-year-old girl with severe calcinosis cutis who developed cutaneous ulceration, rash and myopathy. Observation: Myopathic changes in EMG, muscle edema in MRI, elevated muscle enzymes and Jo-1 positive antibodies. Outcome: Treatment with prednisolone and methotrexate resulted in improvement of the lesion. Message: Calcinosis cutis may be a presenting feature of juvenile dermatomyositis even in the absence of characteristic findings of rash and weakness.
Description
Keywords
Calcification, Dermatomyositis, Diagnosis
Citation
Meher Bijay Kumar, Mishra Pravakar, Sivaraj Pradeep, Padhan Prasanta. Severe Calcinosis Cutis with Cutaneous Ulceration in Juvenile Dermatomyositis. Indian Pediatrics. 2014 Nov; 51(11): 925-927.