Severe Calcinosis Cutis with Cutaneous Ulceration in Juvenile Dermatomyositis.
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Date
2014-11
Journal Title
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Abstract
Background: Calcinosis cutis is usually seen in long standing and untreated cases of
juvenile dermatomyositis. Case characteristics: 7-year-old girl with severe calcinosis cutis
who developed cutaneous ulceration, rash and myopathy. Observation: Myopathic
changes in EMG, muscle edema in MRI, elevated muscle enzymes and Jo-1 positive
antibodies. Outcome: Treatment with prednisolone and methotrexate resulted in
improvement of the lesion. Message: Calcinosis cutis may be a presenting feature of
juvenile dermatomyositis even in the absence of characteristic findings of rash and
weakness.
Description
Keywords
Calcification, Dermatomyositis, Diagnosis
Citation
Meher Bijay Kumar, Mishra Pravakar, Sivaraj Pradeep, Padhan Prasanta. Severe Calcinosis Cutis with Cutaneous Ulceration in Juvenile Dermatomyositis. Indian Pediatrics. 2014 Nov; 51(11): 925-927.