Pediatric and Adolescent Pheochromocytoma: Clinical Presentation and Outcome of Surgery.
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Date
2014-04
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Abstract
Objectives: To describe the clinical presentation and outcome
of surgery in children with pheochromocytoma in a tertiary care
hospital in India.
Methods: Clinical records of 24 children who were operated
between January 1990 and January 2011 were reviewed. The
diagnosis of familial disease was established based on clinical
examination and follow-up events.
Results: Familial, bilateral, extra-adrenal and malignant
pheochromocytoma were observed in 20.8%, 20.8%, 12.5% and
4.2% children, respectively. Median follow-up duration was 36
months. Persistent hypertension was noted in 12.5% patients
and similar proportion died in follow-up.
Conclusions: In the absence of routine genetic screening, good
history and long- term follow up are essential to rule out familial
pheochromocytoma.
Description
Keywords
Adrenal medullary tumor, Secondary hypertension
Citation
Mishra Anjali, Mehrotra Prateek Kumar, Agarwal Gaurav, Agarwal Amit, Mishra Saroj Kanta. Pediatric and Adolescent Pheochromocytoma: Clinical Presentation and Outcome of Surgery. Indian Pediatrics. 2014 Apr; 51(4): 299-302.