Combined pulmonary fibrosis and emphysema with pulmonary arterial hypertension: A Rare Case Report.
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Date
2015-03
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Abstract
Combined pulmonary fi brosis and emphysema (CPFE) is a recently recognized radiologically defi ned syndrome characterized by simultaneous
coexistence of both upper lobe emphysema and lower lobe pulmonary fi brosis.
We present a case of CPFE in a 57-year-old male smoker who presented with dry cough, progressive breathlessness, and swelling of feet. His
chest X-ray revealed bilateral lower Zone reticulonodular opacities with hyperlucent upper Zones. Pulmonary function tests showed wellpreserved
lung volumes and reduced diff using capacity of the lung for carbon monoxide. High-resolution computed tomogram showed bilateral
lower lobe subpleural honeycombing along with fi brosis and traction bronchiectasis with bilateral upper lobe emphysema predominantly
paraseptal type. His 2D echo was suggestive of moderate pulmonary arterial hypertension.
Description
Keywords
Combined pulmonary fibrosis and emphysema, Diffusing capacity of the lung for carbon monoxide, High-resolution computed tomogram, Pulmonary arterial hypertension
Citation
Vipparthi Surya Kumari, Raghumanda Sunil Kumar, Gorantla Sambasiva Rao, Kona Muralidhara Reddy, Jakka Sushmitha. Combined pulmonary fibrosis and emphysema with pulmonary arterial hypertension: A Rare Case Report. IJSS Case Reports & Reviews. 2015 Mar; 1(10): 45-48.