Pulmonary Capillary Haemangiomatosis: A Rare Cause of Pulmonary.
Loading...
Date
2014-10
Authors
Journal Title
Journal ISSN
Volume Title
Publisher
Abstract
Pulmonary capillary haemangiomatosis (PCH) is a rare disorder of unknown aetiology, characterised by proliferating
capillaries that invade the pulmonary interstitium, alveolar septae and the pulmonary vasculature. It is often mis-diagnosed
as primary pulmonary hypertension and pulmonary veno-occlusive disease. Pulmonary capillary haemangiomatosis is a
locally aggressive benign vascular neoplasm of the lung. We report the case of a 19-year-old female who was referred to
us in the early post-partum period with severe pulmonary artery hypertension, which was diagnosed as PCH by open
lung biopsy.
Description
Keywords
Pulmonary capillary haemangiomatosis, Pulmonary hypertension
Citation
Babu K A, Supraja K, Singh R B. Pulmonary Capillary Haemangiomatosis: A Rare Cause of Pulmonary. The Indian Journal of Chest Diseases and Allied Sciences, 2014 Oct; 56 (4): 259-262.