Primary intestinal lymphangiectasia.

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Date
2009-10
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Abstract
Primary intestinal lymphangiectasia (PIL) is a rare disease of intestinal lymphatics presenting with hypoproteinemia, bilateral lower limb edema, ascites, and protein losing enteropathy . We report a series of 4 children from Chennai, India presenting with anasarca, recurrent diarrhea, hypoproteinemia and confirmatory features of PIL on endoscopy and histopathology.
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Keywords
Hypoproteinemia, Intestinal lymphangiectasia, Protein losing enteropathy, Waldmann’s disease
Citation
Suresh N, Ganesh R, Sankar Janani, Sathiyasekaran Malathi. Primary intestinal lymphangiectasia. Indian Pediatrics. 2009 Oct; 46(10): 903-906.