End-stage renal failure in children with autosomal dominant polycystic kidney disease.

Abstract
Clinical presentaiton of autosomal dominant polycystic kidney disease in childhood is uncommon. When present, it is most commonly abdominal mass. Some children may present with hypertension, hematuria, or abdominal pain without enlargement kidneys but renal failure is rare and has never been reported in Thailand. We report a 10-tear-old Thai boy with end-stage renal failure due to Autosomal dominant polycystic kidney disease diagnosed by renal autopsy.
Description
Keywords
End-stage renal failure, Autosomal dominant polycystic kidney disease
Citation
Vongirad Arun, Sumboonnanonda Achra, Sunthornpoch Vibul, Parichatikanond Paisal. End-stage renal failure in children with autosomal dominant polycystic kidney disease. Siriraj Medical Journal, 1994 Apr; 46(4): 293-297.