Clinical and intraoral findings of a patient with tricho-rhino-phalangeal syndrome type I.

Karacay, S; Saygun, I; Tunca, Y; Imirzalioglu, N; Guvenc, G

Clinical and intraoral findings of a patient with tricho-rhino-phalangeal syndrome type I.

Date

2007-03-26

Authors

Abstract

Tricho-rhino-phalangeal syndrome (TRPS) is a rare and an autosomal dominant disorder having the following characteristics: slowly growing sparse hair, medially thick and laterally thin eyebrows, bulbous tip of the nose, long flat philtrum and thin upper lip with vermilion border, protruding ears, cone-shaped epiphyses and swelling. Our report intends to introduce TRPS to the dental literature and to present oral, clinical and radiological data of a patient with TRPS. A rare association of supernumerary teeth was also diagnosed and one of them was extracted as it impeded on the eruption path of left premolar tooth.

Citation

Karacay S, Saygun I, Tunca Y, Imirzalioglu N, Guvenc G. Clinical and intraoral findings of a patient with tricho-rhino-phalangeal syndrome type I. Journal of the Indian Society of Pedodontics and Preventive Dentistry. 2007 Mar; 25(1): 43-5